Successful percutaneous treatment with the Konar MF (TM)-VSD Occluder in an infant with Abernethy syndrome-case report

Loureiro, Petra; Georgiev, Stanimir; Ewert, Peter; Tanase, Daniel; Eicken, Andreas; Kammer, Birgit und Dalla-Pozza, Robert (2021): Successful percutaneous treatment with the Konar MF (TM)-VSD Occluder in an infant with Abernethy syndrome-case report. In: Cardiovascular Diagnosis and Therapy, Bd. 11, Nr. 2: S. 631-636

Abstract

Cyanosis persisting after surgical repair of complex congenital heart disease (CHD) may be related to the underlying disease. However, extracardiac causes should be also considered. We report on a patient with heterotaxy syndrome and double outlet right ventricle, in whom postoperative cyanosis was associated with an Abernethy malformation type II causing a hepatopulmonary syndrome. Despite this complex anatomy, interventional closure of the portosystemic shunt was done with a Konar MF (TM)-VSD Occluder. The patient recovered rapidly with relief of cyanosis within one month. This case highlights the importance of a careful diagnostic assessment in patients with complex CHD, who presents cyanoses after surgical repair. In addition, it shows the feasibility and safety of a percutaneous approach with complete closure of the vascular malformation in a patient with a complex anatomy.

• Dokumententyp: Zeitschriftenartikel
• Fakultät: Medizin
• Themengebiete: 600 Technik, Medizin, angewandte Wissenschaften > 610 Medizin und Gesundheit
• ISSN: 2223-3652
• Sprache: Englisch